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Case Reports
. 2022 Feb 15;15(2):e247229.
doi: 10.1136/bcr-2021-247229.

Coats-like exudative vitreoretinopathy (CLEVER) in CEP290 inherited retinal degeneration

Ann O'Connell  1   2 , Kirk A J Stephenson  3   2 , Julia Zhu  2 , Susan FitzSimon  1
Affiliations
Case Reports

Coats-like exudative vitreoretinopathy (CLEVER) in CEP290 inherited retinal degeneration

Ann O'Connell et al. BMJ Case Rep. .
No abstract available

Keywords: genetics; ophthalmology; retina.

PubMed Disclaimer

Conflict of interest statement

Competing interests: None declared.

Figures

Figure 1
Figure 1
RetCam images (Clarity Medical Systems, USA). (A) Colour fundus photograph of the left eye showing rod-cone dystrophy (RCD) features (bone spicule-like pigmentation, arteriolar attenuation, waxy optic disc pallor) and extensive inferotemporal retinal/subretinal exudation. (B) Fluorescein angiography showing lightbulb telangiectatic vessels within the area of exudate. (C) Colour fundus photograph of the right eye showing RCD features without evidence of exudation.
Figure 2
Figure 2
Colour fundus photographs of the affected inferotemporal fundus showing the interval regression of exudation from before (A) and after (B) treatment with exudate retreating from the macular arcades. Note stigmata of cryotherapy and laser.
See this image and copyright information in PMC

References

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