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. 2022 Jan;118(1):106-109.
doi: 10.36660/abc.20210062.

Long-Term Cardiac Complications of PRKAG2 Syndrome

[Article in English, Portuguese]
Luiz Pereira de Magalhães  1 , Eduardo Faria Soares de Magalhães  2 , Jussara de Oliveira Pinheiro  1 , Alex Teixeira Guabiru  1 , Francisco José Farias Borges Dos Reis  1 , Roque Aras  1
Affiliations

Long-Term Cardiac Complications of PRKAG2 Syndrome

[Article in English, Portuguese]
Luiz Pereira de Magalhães et al. Arq Bras Cardiol. 2022 Jan.
No abstract available

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Conflict of interest statement

Potencial conflito de interesse

Não há conflito com o presente artigo

Figures

Figura 1
Figura 1. Heredograma da família. Indivíduos testados quanto à mutação do PRKAG2: (+) portadores; (-) não portadores da mutação. MP: marca-passo; CDI: cardioversor-desfibrilador implantável; MS: morte súbita.
Figura 2
Figura 2. A) Eletrocardiograma da paciente III:8 mostrando pré-excitação ventricular e morfologia de bloqueio de ramo direito. B) Estudo eletrofisiológico. Intervalo HV= 30 ms. Eletrogramas, A: atrial; H: His; V: ventricular.
Figura 3
Figura 3. Método de Kaplan-Meier: incidência cumulativa de complicações cardiovasculares (implante de marca-passo ou morte súbita).
Figure 1
Figure 1. Genogram of the family. Individuals tested for a PRKAG2 mutation: carriers (+) or non-carriers (-). PM: pacemaker; ICD: implantable cardioverter-defibrillator; SD: sudden death.
Figure 2
Figure 2. A) Electrocardiogram of patient III:8 showing ventricular pre-excitation, and right bundle branch block morphology. B) Electrophysiology study of the same patient. HV interval= 30 ms. Electrograms, A: atrial; H: His bundle; V: ventricular.
Figure 3
Figure 3. Kaplan-Meier curve of the cumulative incidence of cardiovascular events (pacemaker implantation or sudden death).
See this image and copyright information in PMC

References

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