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. 2022 Mar;26(3):226-228.
doi: 10.5152/AnatolJCardiol.2021.465.

Isolated Unilateral Agenesis of Pulmonary Artery and Reappraisal of Embryological Evolution

Jeet Ram Kashyap  1 , Suraj Kumar  1 , Sreenivas Reddy  1 , Raghavendra Rao K  1 , Lipi Uppal  1
Affiliations

Isolated Unilateral Agenesis of Pulmonary Artery and Reappraisal of Embryological Evolution

Jeet Ram Kashyap et al. Anatol J Cardiol. 2022 Mar.
No abstract available

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Figures

Figure 1.
Figure 1.
(A) Electrocardiogram normal except for tachycardia, (B) stress MPI showing a very little ~5% reversible defect in LAD territory, (C) left coronary angiogram showing large collateral arising from LCx and supplying the branches of RPA, (D) systemic collaterals from right internal mammary artery and (E) from the lateral-thoracic artery. (All collaterals shown by white arrows). ECG, electrocardiogram; LCx, left circumflex.
Figure 2.
Figure 2.
(A) The proposed 5 primitive aortic arches, the first and second arch disappear during early fetal life, (B) left aortic arch and absent right pulmonary artery. The proximal part of the terminal arch (herein being referred to as fifth arch) disappears early. The distal part of the terminal aortic arch originates from the innominate artery near its base, and obliterate after birth, leaving the diverticulum of innominate artery, (C) angiogram of the main pulmonary trunk with filling of the left pulmonary artery (LPA) only and complete absence of RPA, (D) volume-rendered 3D reconstruction of multidetector computed tomography (MDCT) image demonstrating the absence of the RPA and (E) MDCT and 3D reconstruction shows diverticulum of the innominate artery. RPA, right pulmonary artery.
See this image and copyright information in PMC

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