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Case Reports
. 2021 Dec 31;27(4):10.7196/AJTCCM.2021.v27i4.128.
doi: 10.7196/AJTCCM.2021.v27i4.128. eCollection 2021.

Bullous lung disease in association with an isolated giant plexiform neuroma: A case report and brief review of pulmonary involvement in neurofibromatosis type 1

M S Shongwe  1 , M J Mpe  1
Affiliations
Case Reports

Bullous lung disease in association with an isolated giant plexiform neuroma: A case report and brief review of pulmonary involvement in neurofibromatosis type 1

M S Shongwe et al. Afr J Thorac Crit Care Med. .

Abstract

Neurofibromatosis is common. It can be accompanied by abnormalities related to the thorax. These vary in severity and can be life-threatening. We present a case of plexiform neuroma with associated extensive bullous lung disease.

Keywords: bullous lung disease; isolated plexiform neuroma.

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Conflict of interest statement

Conflicts of interest: None.

Figures

Fig. 1
Fig. 1
Coronal cut showing extensive bullous changes.
Fig. 2
Fig. 2
Coronal chest computed tomography cut showing marked dilatation of pulmonary arteries.
See this image and copyright information in PMC

References

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