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Case Reports
. 2022 Mar 16:9:814897.
doi: 10.3389/fsurg.2022.814897. eCollection 2022.

Congenital Cutis Laxa: A Case Report and Literature Review

Yang Kun  1 , Shi Mengdong  1 , Fu Cong  2 , Huo Ran  1   2
Affiliations
Case Reports

Congenital Cutis Laxa: A Case Report and Literature Review

Yang Kun et al. Front Surg. .

Abstract

Cutis Laxa is a rare connective tissue disease featuring inelastic and saggy skin. It is thought that plastic surgery might be the most effective treatment, while the previous pieces of literature on the surgical treatment for Cutis Laxa complained of the recurrence. We report a patient of Congenital Cutis Laxa who has received systematic and sequential treatment based on plastic surgery. The patient is content with the effect of treatment, and there are no signs of recurrence after 5 months. By referring to relevant pieces of literature, we evaluate the clinical manifestations and diagnosis of the disease. A multi-step, systematic, and sequential treatment is recommended for the treatment of Congenital Cutis Laxa.

Keywords: Congenital Cutis Laxa; plastic surgery; recurrence; sequential treatment; systematic treatment.

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Conflict of interest statement

The authors declare that the research was conducted in the absence of any commercial or financial relationships that could be construed as a potential conflict of interest.

Figures

Figure 1
Figure 1
Pre-operative frontal and oblique views.
Figure 2
Figure 2
Post-operative frontal and oblique views for 5 months after the surgery.
Figure 3
Figure 3
Absence or significant reduction of elastic fibers in the dermis layer and residual fragments of elastic fibers (elastic fiber staining × 400).
See this image and copyright information in PMC

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