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. 2019 Feb;4(1):77-78.
doi: 10.1177/2397198318798588. Epub 2018 Sep 21.

The prevalence of localised scleroderma in childhood assessed in the administrative claims data from the United States

Timothy Beukelman  1 , Fenglong Xie  2 , Ivan Foeldvari  3
Affiliations

The prevalence of localised scleroderma in childhood assessed in the administrative claims data from the United States

Timothy Beukelman et al. J Scleroderma Relat Disord. 2019 Feb.

Abstract

Juvenile localised scleroderma is believed an orphan autoimmune disease, which occurs 10 times more often than systemic sclerosis in childhood and is believed to have a prevalence of 1 per 100,000 children. To gain data regarding the prevalence of juvenile localised scleroderma, we assessed the administrative claims data in the United States using the International Classification of Diseases, Ninth Revision diagnosis codes. We found an estimated prevalence in each year ranging from 3.2 to 3.6 per 10,000 children. This estimate is significantly higher as found in previous studies.

Keywords: Localised scleroderma; prevalence.

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Conflict of interest statement

Declaration of conflicting interests: The author(s) declared no potential conflicts of interest with respect to the research, authorship and/or publication of this article.

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