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. 2018 Jun;3(2):189-190.
doi: 10.1177/2397198318763701. Epub 2018 Mar 27.

Assessing the prevalence of juvenile systemic sclerosis in childhood using administrative claims data from the United States

Timothy Beukelman  1 , Fenglong Xie  2 , Ivan Foeldvari  3
Affiliations

Assessing the prevalence of juvenile systemic sclerosis in childhood using administrative claims data from the United States

Timothy Beukelman et al. J Scleroderma Relat Disord. 2018 Jun.

Abstract

Juvenile systemic sclerosis is a very rare orphan disease. To date, only one publication has estimated the prevalence of juvenile systemic sclerosis using a survey of specialized physicians. We conducted a study of administrative claims data in the United States using the International Classification of Diseases, Ninth Revision diagnosis codes and found a prevalence of approximately 3 per 1,000,000 children. This estimate will inform the planning of prospective studies.

Keywords: Prevalence; juvenile systemic sclerosis.

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Conflict of interest statement

Declaration of conflicting interests: The author(s) declared no potential conflicts of interest with respect to the research, authorship, and/or publication of this article.

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