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Case Reports
. 2022 Jul 1;44(5):e881-e883.
doi: 10.1097/MPH.0000000000002444. Epub 2022 Apr 1.

Idiopathic Hypereosinophilic Syndrome Associated With Pulmonary Hypertension in an Infant

Yunus M Akcabelen  1 , Gökçe Kaya Dinçel  2 , İbrahim Ece  2 , Güzin Cinel  3 , Turan Bayhan  4 , Namik Y Özbek  1
Affiliations
Case Reports

Idiopathic Hypereosinophilic Syndrome Associated With Pulmonary Hypertension in an Infant

Yunus M Akcabelen et al. J Pediatr Hematol Oncol. .

Abstract

Hypereosinophilic syndrome (HES) is a very rare disease during childhood. It involves the different organs like skin, gastrointestinal system, heart and lungs, besides pulmonary hypertension (PHT) is a very rare morbidity of HES that may cause life-threatening complications. PHT improves with the treatment of hypereosinophilia, without the need for pulmonary vasodilator therapy. Here, we present a case of PHT developed after recovery of pulmonary infiltration in an infant with idiopathic HES. We revealed that pulmonary pressure returned to normal range in parallel with the decrease in eosinophil count with steroid treatment.

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Conflict of interest statement

The authors declare no conflict of interest.

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