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. 2022 Apr 1:20:eRW5686.
doi: 10.31744/einstein_journal/2022RW5686. eCollection 2022.

Brazilian Guidelines for Nutrition in Cystic Fibrosis

Lenycia de Cassya Lopes Neri  1 , Miriam Isabel Souza Dos Santos Simon  2 , Valéria Laguna Salomão Ambrósio  3 , Eliana Barbosa  4 , Monique Ferreira Garcia  4 , Juliana Ferreira Mauri  5 , Renata Rodrigues Guirau  6 , Mirella Aparecida Neves  7 , Carolina de Azevedo Pedrosa Cunha  8 , Marcelo Coelho Nogueira  9 , Anna Carolina Di Creddo Alves  10 , Jocemara Gurmini  7 , Maria de Fatima Servidoni  6 , Matias Epifanio  11 , Rodrigo Athanazio  10 ; Grupo de Trabalho das Diretrizes Brasileiras de Nutrição em Fibrose Cística
Affiliations

Brazilian Guidelines for Nutrition in Cystic Fibrosis

Lenycia de Cassya Lopes Neri et al. Einstein (Sao Paulo). .

Abstract

Objective: To develop a scientific consensus on nutrition in cystic fibrosis.

Methods: Sixteen coordinators elaborated relevant questions on nutritional therapy in cystic fibrosis, which were divided into six sections: nutritional assessment, nutritional recommendations, nutritional intervention, dietary counseling, special situations and enzyme replacement, and gastrointestinal manifestations. Two to three specialists in the field were responsible for each section and obtaining answers formulated based on standardized bibliographic searches. The available literature was searched in the PubMed®/MEDLINE database, after training and standardization of search strategies, to write the best level of evidence for the questions elaborated. Issues related to disagreement were discussed until a consensus was reached among specialists, based on the current scientific literature.

Results: Forty-two questions were prepared and objectively answered, resulting in a consensus of nutritional therapy in cystic fibrosis.

Conclusion: This work enabled establishing a scientific consensus for nutritional treatment of cystic fibrosis patients.

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References

    1. Sinaasappel M, Stern M, Littlewood J, Wolfe S, Steinkamp G, Heijerman HG, et al. Nutrition in patients with cystic fibrosis: a European Consensus. J Cyst Fibros. 2002;1(2):51-75. Review. - PubMed
    1. Sanders DB, Fink A, Mayer-Hamblett N, Schechter MS, Sawicki GS, Rosenfeld M, et al. Early life growth trajectories in cystic fibrosis are associated with pulmonary function at age 6 years. J Pediatr. 2015;167(5):1081-8. e1. - PMC - PubMed
    1. Corey M, McLaughlin FJ, Williams M, Levison H. A comparison of survival, growth, and pulmonary function in patients with cystic fibrosis in Boston and Toronto. J Clin Epidemiol. 1988;41(6):583-91. - PubMed
    1. Turck D, Braegger CP, Colombo C, Declercq D, Morton A, Pancheva R, et al. ESPEN-ESPGHAN-ECFS guidelines on nutrition care for infants, children, and adults with cystic fibrosis. Clin Nutr. 2016;35(3):557-77. - PubMed
    1. Sermet-Gaudelus I, Mayell SJ, Southern KW; European Cystic Finrosis Society (ECFS), Neonatal Screening Working Group. Guidelines on the early management of infants diagnosed with cystic fibrosis following newborn screening. J Cyst Fibros. 2010;9(5):323-9. - PubMed