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Case Reports
. 2022 Mar 2;15(1):89-91.
doi: 10.4103/ojo.ojo_348_20. eCollection 2022 Jan-Apr.

Tractional retinal detachment and juxtapapillary retinal capillary hemangioma in a 6-year-old girl: A case report

Franco Benvenuto  1 , Mariana Sgroi  1 , Gabriela Lamas  2 , Luis Diaz Gonzalez  1 , Adriana Fandiño  1
Affiliations
Case Reports

Tractional retinal detachment and juxtapapillary retinal capillary hemangioma in a 6-year-old girl: A case report

Franco Benvenuto et al. Oman J Ophthalmol. .

Abstract

A 6-year-old girl with visual impairment in the right eye (OD) was referred for an eye evaluation. The fundus of the OD showed a fibrotic orange endophytic lesion located adjacent to the optic disc. In retinal optical coherence tomography, a local tractional retinal detachment and choroidal neovascular membrane were observed together also with the presence of subretinal fluid. Due to the vision of the OD evolved to nonlight perception in the following exam, enucleation was performed. The pathology report was correlated with hemangioblastoma. Herein, we describe a case of a young girl with a retinal hemangioblastoma with quick evolution and without prior systemic diagnosis.

Keywords: Hemangioblastoma; Von Hippel-Lindau; ocular oncology; oncology; pediatric retina.

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Conflict of interest statement

There are no conflicts of interest.

Figures

Figure 1
Figure 1
OD fundus retinography with a fibrotic orange endophytic juxtapapillary lesion
Figure 2
Figure 2
(a) OD optical coherence tomography, macular tractional detachment, and subretinal fluid. (b) OD optical coherence tomography that shows macular tractional detachment with a choroidal neovascular membrane
Figure 3
Figure 3
Magnetic resonance imaging with a total retinal detachment in the OD
Figure 4
Figure 4
(a) Pathology macroscopy examination shows a white-yellowish mass of 1.1 cm × 0.8 cm, and no optic nerve invasion. (b) Histology image with a tumor located in the retina, consisting of small vascular structures, and stromal cells with clear cytoplasm (c) Immunohistochemistry image, vascular structures were positive for CD31
See this image and copyright information in PMC

References

    1. Gass JD. Developmental tumors of the retinal pigment epithelium (RPE) and retina. In: Gass JD, editor. Stereoscopic Atlas of Macular Diseases, Diagnosis and Treatment. 2nd ed. St Louis, Missouri: Mosby; 1997. p. 1061.
    1. Singh AD, Rundle PA, Rennie I. Retinal vascular tumors. Ophthalmol Clin North Am. 2005;18:167–76. - PubMed
    1. Kase S, Ishida S. Retinal capillary hemangioma in von Hippel-Lindau disease: Current concept, diagnosis and managements. J Transl Med Epidemiol. 2014;2:1010.
    1. McCabe CM, Flynn HW, Jr, Shields CL, Shields JA, Regillo CD, McDonald HR, et al. Juxtapapillary capillary hemangiomas. Clinical features and visual acuity outcomes. Ophthalmology. 2000;107:2240–8. - PubMed
    1. Magee MA, Kroll AJ, Lou PL, Ryan EA. Retinal capillary hemangiomas and von Hippel-Lindau disease. Semin Ophthalmol. 2006;21:143–50. - PubMed

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