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Case Reports
. 2021 Oct-Dec;15(4):454-456.
doi: 10.4103/aer.aer_137_21. Epub 2022 Mar 1.

Anesthetic Management in a Case of MURCS Syndrome

Affiliations
Case Reports

Anesthetic Management in a Case of MURCS Syndrome

J R Rekha et al. Anesth Essays Res. 2021 Oct-Dec.

Abstract

MURCS syndrome is a more severe form of Mayer-Rokitansky-Küster-Hauser (MRKH) syndrome, an acronym meaning aplasia/hypoplasia of Müllerian ducts (MU), congenital renal agenesis/ectopia (R), and cervical somite dysplasia (CS). A common presentation is primary amenorrhea in adolescent females. An anesthetist must consider the benefits and limitations of both regional and general anesthesia for these patients based on site of surgery and severity of malformations. We report successful anesthetic management of a 21-year-old female with MURCS syndrome scheduled for a creation of neovagina under spinal anesthesia using ultrasound guidance.

Keywords: Amenorrhea; Klippel–Feil; MURCS syndrome; Mayer-Rokitansky-Küster-Hauser syndrome; hemivertebra; scoliosis.

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Conflict of interest statement

There are no conflicts of interest.

Figures

Figure 1
Figure 1
Coronal T2-weighted magnetic resonance image showing absent inferior articular process of L5 on the right side (arrow) and fusion of L5–S1 articular processes on the left side (white asterisk)
Figure 2
Figure 2
Coronal T2 magnetic resonance imaging of thoracolumbar spine reveals the presence of scoliosis at lower lumbar level with convexity toward the right (arrow)

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