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. 2022 Aug 16;37(4):591-594.
doi: 10.21470/1678-9741-2021-0323.

Lutembacher Syndrome with Sinus Venosus-Type Interatrial Communication: An Educational Presentation

Andréa Bezerra de Melo da Silveira Lordsleem  1 , Sandro Gonçalves de Lima  1 , Lucas Soares Bezerra  2 , Eveline Barros Calado  1 , Fabio Antônio Amando Granja  1 , Brivaldo Markman-Filho  1
Affiliations

Lutembacher Syndrome with Sinus Venosus-Type Interatrial Communication: An Educational Presentation

Andréa Bezerra de Melo da Silveira Lordsleem et al. Braz J Cardiovasc Surg. .
No abstract available

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Conflict of interest statement

No conflict of interest.

Figures

Fig. 1
Fig. 1. Eletrocardiogram demonstrating atrial fibrillation with an axis deviation to the right.
Fig. 2
Fig. 2. Transthoracic echocardiogram demonstrating an opening in the dome of the mitral valve with significant mitral stenosis, biatrial and right ventricular enlargements, moderate/significant tricuspid insufficiency, mild pulmonary arterial hypertension and pericardial effusion.
Fig. 3
Fig. 3. Angiotomography demonstrating: A - mitral valve with thickened leaflets and reduced opening (valve area 0.6 cm2); B - a significantly enlarged biatrial and of the right ventricle; C - a significantly enlarged of the inferior vena cava and D - a large pericardial effusion.
Fig. 4
Fig. 4. In A we observe a significant enlargement of the right chambers and the superior vena cava. In B we may observe the sinus venosus-type IAC.
Fig. 5
Fig. 5. Cranial computed tomography scan with lesions suggestive of chronic ischemia in the left parietal, temporal and frontal lobes.
See this image and copyright information in PMC

References

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