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Case Reports
. 2022 Mar 27;58(4):484.
doi: 10.3390/medicina58040484.

Paraneoplastic Wong-Type Dermatomyositis Associated with Gynecological Malignancy

Roberto Russo  1   2 , Giulia Gasparini  1   2 , Emanuele Cozzani  1   2 , Brunella Gravina  3 , Aurora Parodi  1   2
Affiliations
Case Reports

Paraneoplastic Wong-Type Dermatomyositis Associated with Gynecological Malignancy

Roberto Russo et al. Medicina (Kaunas). .

Abstract

Although dermatomyositis is known to be a possible paraneoplastic syndrome, often in the setting of gynecological cancers, Wong-type dermatomyositis-a rare variant of dermatomyositis-has not been clearly associated with internal malignancies to date. There is only one report from Japan of a woman who developed Wong-type dermatomyositis together with the recurrence of uterine cancer. We report the case of a Caucasian patient who presented with infrequent Wong-type dermatomyositis with positive anti-TIF1γ antibodies; screening for internal malignancies revealed fallopian tube carcinoma.

Keywords: Wong-type dermatomyositis; dermatomyositis; paraneoplastic skin diseases.

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Conflict of interest statement

The authors declare no conflict of interest.

Figures

Figure 1
Figure 1
(A) Palpebral edema; heliotropic erythema of face, neck, chest, shoulder and arms. (B) Particular of hyperkeratotic, erythematous, follicular confluent papules arranged in a linear fashion on forearm.
Figure 2
Figure 2
Close-up view of palpebral heliotropic erythema.
See this image and copyright information in PMC

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