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Case Reports
. 2022 Apr 22:2022:9585460.
doi: 10.1155/2022/9585460. eCollection 2022.

Dental Management of a Tunisian Child with Sanjad-Sakati Syndrome

Farah Chouchene  1 , Aymen Ben Haj Khalifa  1   2 , Fatma Masmoudi  1 , Ahlem Baaziz  1 , Fethi Maatouk  1 , Hichem Ghedira  1
Affiliations
Case Reports

Dental Management of a Tunisian Child with Sanjad-Sakati Syndrome

Farah Chouchene et al. Case Rep Dent. .

Abstract

Sanjad-Sakati syndrome (SSS) is a rare autosomal recessive congenital disorder. The present case report is aimed at describing the orofacial manifestations and dental management of a 4-year seven-month-old, Tunisian boy with SSS. The patient has typical dysmorphic facial features and growth retardation. Intraoral examination revealed micrognathic mandible and maxilla, an arched palate, and small dental arches with an open bite. All the maxillary and mandibular teeth were decayed due to the poor oral hygiene, plaque accumulation, and enamel hypoplasia. Oral rehabilitation involved pulpotomies and root canal therapies on decayed teeth. Resin composite restorations were performed on maxillary and mandibular incisors, and stainless-steel crowns were placed on maxillary and mandibular first and second primary molars. Dental treatment of children with SSS should improve their quality of life and their general health. Undeveloped dental arches associated with dental anomalies as well as learning deficit make very difficult of the oral rehabilitation of such patients.

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Conflict of interest statement

None of the authors has declared any conflict of interest or financial disclosures.

Figures

Figure 1
Figure 1
Head and neck examination.
Figure 2
Figure 2
Intraoral view (preoperative features).
Figure 3
Figure 3
Postoperative restorative treatments.
See this image and copyright information in PMC

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