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. 2022 May-Jun;12(3):370-375.
doi: 10.1016/j.jobcr.2022.04.002. Epub 2022 Apr 28.

Apert Syndrome: Dental management considerations and objectives

Line Droubi  1 , Mohannad Laflouf  1 , Yasser Alsayed Tolibah  1 , John C Comisi  2
Affiliations

Apert Syndrome: Dental management considerations and objectives

Line Droubi et al. J Oral Biol Craniofac Res. 2022 May-Jun.

Abstract

Background: Apert syndrome (AS) is a rare congenital disorder that correlates with many craniofacial features, like craniosynostosis, midfacial malformation, and symmetrical syndactyly of the hands and feet.

Aim: This paper describes the facial and oral manifestations in a 20-year-old female previously diagnosed with AS, discusses the complex dental treatment plan and treatments, including the use of a customized toothbrush handle to enhance the patient's brushing ability.

Results: A satisfactory outcome was provided, and the patients quality of life improved significantly due to this comprehensive multi-disciplinary care process.

Conclusions: Comprehensive examination, extensive medical history reviewed, parental and patient consent are needed to establish a comprehensive treatment plan regarding the special needs of these patients.

Keywords: Apert syndrome; Craniosynostosis; Customized handle for toothbrush; Dental care; Syndactyly.

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Conflict of interest statement

The authors declare no conflict of interest.

Figures

Image 1
Graphical abstract
Fig. 1
Fig. 1
(A) Frontal view of the patient. (B) Lateral view of the patient (C) The patient hands that treated previously. (D) Bilateral symmetrical syndactyly of both the feet.
Fig. 2
Fig. 2
(A) Occlusal view of maxilla. (B) Occlusal view mandibular. (C) Frontal view of both arches in occlusion.
Fig. 3
Fig. 3
A panoramic radiograph showing Impacted teeth # 14-27, extremely large carious lesions teeth # 11,21,33,43 and superficial carious lesion teeth # 44-45-46.
Fig. 4
Fig. 4
(A) Patient in closed hand position. (B) Patient grasping a conventional toothbrush. (C) Recording patient's grip impression by using Poly Siloxane material.
Fig. 5
Fig. 5
A periapical radiograph for root canal treatment teeth # 11-21.
Fig. 6
Fig. 6
(A) Restorative treatment on teeth # 44-45-46 and sealant applied on tooth # 47. (B) Extracted teeth # 11,21. (C-D) Sealant applied on teeth # 13-14-16-18-24-25-26-28-34-35-37-38. (E) Frontal view of restored dentition.
See this image and copyright information in PMC

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