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Case Reports
. 2022 May 10;20(1):35.
doi: 10.1186/s12969-022-00693-8.

The use of ECMO in pediatric granulomatosis with polyangiitis

Rachel Finkel  1 , Jesse Honig  2 , Chun P Chao  3 , Erin Rescoe  4 , Sonia Solomon  5
Affiliations
Case Reports

The use of ECMO in pediatric granulomatosis with polyangiitis

Rachel Finkel et al. Pediatr Rheumatol Online J. .

Abstract

Background: Granulomatosis with polyangiitis (GPA) vasculitis with pulmonary-renal syndrome rarely presents in children and is associated with high mortality rates.

Case presentation: We present the case of a 13-year-old male with newly diagnosed GPA vasculitis, treated with extracorporeal membrane oxygenation, continuous renal replacement therapy, plasmapheresis, rituximab, cyclophosphamide, and corticosteroids.

Conclusion: This case presentation demonstrates that ECMO can be used as a life supporting therapy in pediatric patients with pulmonary hemorrhage from ANCA vasculitis in conjunction with other therapies.

Keywords: AAV; ANCA; ECMO; HD; Vasculitis.

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Conflict of interest statement

The authors declare that they have no competing interests.

References

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