Thoracic Ewing's Sarcoma: A Case Report

Abstract

Ewing's sarcoma family of tumors (ESFTs) contains multiple tumors with similar histological and immunohistochemical features. ESFTs are small, round cell, highly malignant tumors that arise from the neuroectoderm of bone and extraskeletal soft tissue. Ewing's sarcoma is the second most common primary malignant bone cancer in children and adolescents, with the second decade of life being the most common age of diagnosis. In this article, we present a case of a young male who presented to the emergency department complaining of shortness of breath and cough and was later diagnosed with Ewing's sarcoma of the chest wall, which is also called Askin's tumor, and it is an extremely rare disease with only 17 cases reported in the literature.

Keywords: askin’s tumor; ewing’s sarcoma; extraosseous ewing’s sarcoma; primitive neuroectodermal tumor; thoracic ewing’s sarcoma.

Figure 1. Chest X-ray showing a large mass (yellow circle) in the right hemithorax with a mediastinal and tracheal shift to the left.

Figure 2. Chest CT scan showing a 15 × 12 × 16 cm mass (yellow circle) extending into the chest wall and right axilla with heterogeneous enhancement and occupying the middle and upper right hemithorax.

Figure 3. Pathology slide showing areas of tumor necrosis (yellow arrow).

Figure 4. Pathology slide showing small, round, blue cells arranged in a solid pattern with the formation of occasional, vague rosettes (yellow circle).