Skip to main page content
U.S. flag

An official website of the United States government

Dot gov

The .gov means it’s official.
Federal government websites often end in .gov or .mil. Before sharing sensitive information, make sure you’re on a federal government site.

Https

The site is secure.
The https:// ensures that you are connecting to the official website and that any information you provide is encrypted and transmitted securely.

Access keys NCBI Homepage MyNCBI Homepage Main Content Main Navigation
Case Reports
. 2022 May 10:43:102109.
doi: 10.1016/j.eucr.2022.102109. eCollection 2022 Jul.

Urachal rhabdomyosarcoma: A case report of an extremely rare localisation

Amina Karray  1 , Sondos Sahli  1 , Zohra Rahal  1 , Bochra Aziza  1 , Riadh Jouini  1
Affiliations
Case Reports

Urachal rhabdomyosarcoma: A case report of an extremely rare localisation

Amina Karray et al. Urol Case Rep. .

Abstract

Urachus is a tubular structure connecting the allatois to the bladder's apex, in the embryonic development. We report a rare case of a 5-year-old boy, with no past medical history, complaining of secondary enuresis, pollakiuria and urgent incontinence. Physical exam revealed a hypogastric mass. Echo guided percutaneous biopsy followed by a histological analysis showed embryonal RMS. The remainder of the staging ruled out metastasis. The patient received neoadjuvant chemotherapy before proceeding to complete tumor excision. Surgical exploration revealed that the tumor was primitively related to the urachus. Total resection was performed. The one year follow-up was uneventful.

Keywords: Oncology; Pediatrics; Rhabdomyosarcoma (RMS); Urachus.

PubMed Disclaimer

Conflict of interest statement

The authors declare that there are no conflicts of interest regarding the publication of this article.

Figures

Fig. 1
Fig. 1
Tumoral cells showed positive myogenic (a) desmin (b) markers in histopathology.
Fig. 2
Fig. 2
Pelvic MRI large anterior medial mass displacing the bladder.
See this image and copyright information in PMC

References

    1. Gartrell J., Pappo A. Recent advances in understanding and managing pediatric rhabdomyosarcoma. F1000Res. 2020 Jul 8:9. - PMC - PubMed
    1. Cheikhelard A., Irtan S., Orbach D., et al. Urachal rhabdomyosarcoma in childhood: a rare entity with a poor outcome. J Pediatr Surg. 2015 Aug;50(8):1329–1333. - PubMed
    1. Orbatu D., Alaygut D. Evaluation and management of urachal remnants in children. Pediatr Int. 2020 Oct;62(10):1158–1161. - PubMed
    1. Mylonas K.S., O Malley P., Ziogas I.A., El-Kabab L., Nasioudis D. Malignant urachal neoplasms: a population-based study and systematic review of literature. Urol Oncol. 2017 Jan;35(1):33.e11–33.e19. - PubMed
    1. Stevens M.C.G., Rey A., Bouvet N., et al. Treatment of nonmetastatic rhabdomyosarcoma in childhood and adolescence: third study of the International Society of Paediatric Oncology--SIOP malignant mesenchymal tumor 89. J Clin Oncol. 2005 Apr 20;23(12):2618–2628. - PubMed

Publication types

LinkOut - more resources