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. 2022 Jul 15;62(7):307-312.
doi: 10.2176/jns-nmc.2022-0072. Epub 2022 May 25.

Diagnostic Criteria for Moyamoya Disease - 2021 Revised Version

Satoshi Kuroda  1 , Miki Fujimura  2 , Jun Takahashi  3 , Hiroharu Kataoka  4 , Kuniaki Ogasawara  5 , Toru Iwama  6 , Teiji Tominaga  7 , Susumu Miyamoto  8 ; Research Committee on Moyamoya Disease (Spontaneous Occlusion of Circle of Willis) of the Ministry of Health, Labor, and Welfare, Japan
Affiliations

Diagnostic Criteria for Moyamoya Disease - 2021 Revised Version

Satoshi Kuroda et al. Neurol Med Chir (Tokyo). .

Abstract

In this report, we, the Research Committee on Moyamoya Disease (Spontaneous Occlusion of the circle of Willis), describe in detail the changes in the new "Diagnostic Criteria 2021" for moyamoya disease and its scientific basis to make it widely known to the world. The revised criteria cover all aspects of the disease, including a definition of the disease concept, diagnostic imaging, and the concept of quasi-moyamoya disease (moyamoya syndrome).

Keywords: MRI; cerebral angiography; diagnostic criteria; moyamoya disease.

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Conflict of interest statement

There is no COI to be disclosed. All authors have registered online self-reported COI Disclosure Statement Form through the website for JNS members.

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Supplementary concepts