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. 2022 Jun 6;79(2):193-196.
doi: 10.31053/1853.0605.v79.n2.32922.

[Dilated cardiomyopathy in a patient with Eosinophilic Granulomatosis with Polyangiitis (Churg Strauss)]

[Article in Spanish]
Julieta Lozita  1 , Judith Mailén Vicentín  2 , María Florencia Melgarejo Otarola  3 , Jorge Andrés Paolasso  4 , Roberto Miguel Angel Colque  5 , Pablo Ezequiel Sarmiento  6
Affiliations

[Dilated cardiomyopathy in a patient with Eosinophilic Granulomatosis with Polyangiitis (Churg Strauss)]

[Article in Spanish]
Julieta Lozita et al. Rev Fac Cien Med Univ Nac Cordoba. .

Abstract
in English, Spanish

Eosinophilic granulomatosis with polyangiitis, formerly known as Churg-Strauss Syndrome, is a rare pathology that belongs to the group of diseases characterized by necrotizing vasculitis of small and medium-sized systemic blood vessels. Symptomatic cardiovascular involvement occurs in 27% to 47% of Churg-Strauss cases, being one of the most serious manifestations. The diagnosis is usually confirmed with tissue biopsy showing eosinophil infiltration, but in selected cases with the recent inclusion of cardiac MRI, we can dispense with it. Early diagnosis is important because early treatment is usually associated with improvement in the condition.

La granulomatosis eosinofílica con poliangeítis, anteriormente conocida como síndrome de Churg-Strauss, es una patología poco frecuente que pertenece al grupo de enfermedades caracterizadas por vasculitis necrotizante de vasos sanguíneos sistémicos de pequeño y mediano calibre. La afectación cardiovascular sintomática ocurre entre un 27% a un 47% de los casos de Churg-Strauss, siendo una de las manifestaciones más graves. El diagnóstico suele confirmarse con biopsia de tejido con infiltración de eosinófilos, pero con la reciente inclusión de la resonancia cardíaca, podemos prescindir de ella. El diagnóstico precoz es importante debido a que el tratamiento oportuno suele asociarse con mejoría del cuadro.

Keywords: cardiomyopathy, dilated; churg-strauss syndrome; heart failure.

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Conflict of interest statement

Conflictos de interés Ninguno

Figures

Figura 1
Figura 1. Secuencias PSIR (realce tardío) en eje cortos donde se observa fibrosis intramiocardica focal en regio septal e interoseptal basales (flechas)
Figura 2
Figura 2. Secuencias PSIR (realce tardío) en eje largos donde se observa fibrosis subendocardica en regio apical (flechas)
See this image and copyright information in PMC

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