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Case Reports
. 2022 Apr 22;13(1):292-296.
doi: 10.1159/000524363. eCollection 2022 Jan-Apr.

Coexistence of Idiopathic Intracranial Hypertension with Unilateral Duane Retraction Syndrome Type 1 in an Adult Female

Abdullah I Almater  1 , Jawaher Jehad Alwatban  2 , Arwa Z Alromaih  1 , Motazz Alarfaj  2   3 , Majed Al-Obailan  1
Affiliations
Case Reports

Coexistence of Idiopathic Intracranial Hypertension with Unilateral Duane Retraction Syndrome Type 1 in an Adult Female

Abdullah I Almater et al. Case Rep Ophthalmol. .

Abstract

Idiopathic intracranial hypertension (IIH) is a poorly understood condition, and its presentation can coexist with other diseases. Simultaneous IIH and Duane retraction syndrome (DRS) type 1 have never been reported to coexist in an adult patient. Herein, we report a 32-year-old obese female with a history of chronic renal failure who had a renal transplant rejection 6 years prior to presentation and was treated with oral steroids and immunosuppressive medications. She began to experience signs and symptoms of increased intracranial pressure (morning headache and binocular horizontal diplopia) and had limited abduction of one eye on examination. The case was later diagnosed as IIH with DRS type 1.

Keywords: Duane retraction syndrome; Idiopathic intracranial hypertension; Pseudotumor cerebri.

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Conflict of interest statement

The authors have no conflicts of interest to declare.

Figures

Fig. 1
Fig. 1
A composite picture of the nine positions of gaze, showing right eye esotropia at primary position, limitation of abduction of the right eye, and narrowing of the palpebral fissure on adduction of the right eye.
Fig. 2
Fig. 2
A side view picture of the right eye showing normal globe position in (a) and globe retraction with narrowing of the palpebral fissure on adduction in (b), compatible with the diagnosis of DRS type 1.
See this image and copyright information in PMC

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