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. 2022 Jul;70(7):2727-2728.
doi: 10.4103/ijo.IJO_2994_21.

Beyond retina in Sjogren-Larsson syndrome

Neelam Pawar  1 , R Meenakshi  1 , Devendra Maheshwari  1 , A Fathima  1 , Sabyasachi Chakrabarty  1 , Mihir Paranjape  1
Affiliations

Beyond retina in Sjogren-Larsson syndrome

Neelam Pawar et al. Indian J Ophthalmol. 2022 Jul.
No abstract available

Keywords: Cataract; Sjogrens–Larsson; crystalline retinopathy.

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Conflict of interest statement

None

Figures

Figure 1
Figure 1
(a and b) The characteristic thickening and hyperpigmentation of axillae, flexion contractures in leg and abdomen, respectively
Figure 2
Figure 2
The clinical photo showing posterior capsular cataract in this patient
Figure 3
Figure 3
(a and b) Fundus photo exhibited intraretinal crystals in the macular region in both eyes along with retinal pigmentary changes and atrophy. (c and d) The autofluorescence images in both eyes showed lack of normal FAF attenuation at the fovea
See this image and copyright information in PMC

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