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Case Reports
. 2022 Jul 4;10(1):e84-e87.
doi: 10.1055/s-0042-1750134. eCollection 2022 Jan.

Emergency Separation of Extreme VLBW Omphalopagus Twins: Case Report

Affiliations
Case Reports

Emergency Separation of Extreme VLBW Omphalopagus Twins: Case Report

Waleed Burhamah et al. European J Pediatr Surg Rep. .

Erratum in

Abstract

The classification of conjoint twins is based according to the site of attachment. The challenges in management of such anomalies span the entire continuum of care from delivery to resuscitation to separation and finally discharge. Scheduled separation is ideal, occasionally the caring team is faced with no option but to perform an emergent separation. Omphalopagus is a type of conjoined twinning characterized by union of the peritoneal cavities through an infraumbilical abdominal wall defect. In this report we describe our experience with a successful emergency separation of extremely preterm omphalopagus twins. This is the first case of conjoint twins in Kuwait, we highlight the challenges faced, stressing the importance of adhering to antenatal care as well as management by a multidisciplinary team.

Keywords: bladder exstrophy; conjoined twins; omphalopagus twins.

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Conflict of interest statement

Conflict of Interest None declared.

Figures

Fig. 1
Fig. 1
The conjoined twins upon initial assessment following birth. Note: the conjoined segment with a dusky segment of small bowel.
Fig. 2
Fig. 2
An intraoperative image demonstrating the small bowel of baby 1 ending distally in the anti-mesenteric boarder of the terminal ileum in Baby 2.
Fig. 3
Fig. 3
An immediate post-operative image of both babies. Note the end ileostomy in baby 1 and an end colostomy with a mucous fistula in baby 2. A vesicostomy was created in both babies.
Fig. 4
Fig. 4
( A and B ) Illustrates a follow-up image at 5 months of age for both babies.
Fig. 5
Fig. 5
( A , B ) Illustrates a follow-up image of age for both babies.

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