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Case Reports
. 2022 Jun;26(6):728-730.
doi: 10.5005/jp-journals-10071-24253.

Porphyria-induced Postpartum Reversible Posterior Encephalopathy Syndrome

Shri R Sharma  1 , Nalini Sharma  1 , Baiakmenlang Synmon  2 , Yasmeen Hynniewtaya  2
Affiliations
Case Reports

Porphyria-induced Postpartum Reversible Posterior Encephalopathy Syndrome

Shri R Sharma et al. Indian J Crit Care Med. 2022 Jun.

Abstract

Acute intermittent porphyria (AIP) is a rare condition that needs to be kept in mind where its early recognition, conservative management, and removal of the precipitating factor are the key factors in its management. This "little imitator" presented with varied symptoms is often misdiagnosed. The diagnosis requires a strong index of suspicion as choosing an antiepileptic medication in the management of seizure requires a judicial choice to avoid precipitation of the underlying illness. How to cite this article: Sharma SR, Sharma N, Synmon B, Hynniewtaya Y. Porphyria-induced Postpartum Reversible Posterior Encephalopathy Syndrome. Indian J Crit Care Med 2022;26(6):728-730.

Keywords: Acute intermittent porphyria; Encephalopathy; Postpartum period; Seizures.

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Conflict of interest statement

Source of support: Nil Conflict of interest: None

Figures

Figs 1A to C
Figs 1A to C
(A) MRI brain axial and FLAIR image showing bilateral symmetrical high-intense signal changes involving parieto-occipital cortex and asymmetrical white matter in bilateral parietal lobes. Corresponding ADC and DWI in (B and C) shows no restriction diffusion RESTR
See this image and copyright information in PMC

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