Orbitocranial fibrous dysplasia. A case report

Abstract

A 14-year-old girl had right proptosis, facial asymmetry, and gradual increasing poor vision. X-ray findings showed sclerosis in the sphenoidal bone and the base of the skull. Partial excision of dysplastic bone, decompression of the optic canal, orbit, and superior orbital fissure, and reconstruction of the upper orbital wall were performed one year later. Histopathologic examinations disclosed fibrous dysplasia of sclerotic form. There has been no progression of the disease since the surgery, and good cosmetic and visual results had been achieved.