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Case Reports
. 2022 Aug 3;10(8):e6122.
doi: 10.1002/ccr3.6122. eCollection 2022 Aug.

Early onset of scleromyxedema Arndt-Gottron associated with a monoclonal gammapathy: Successful treatment with intravenous immunoglobulins

Asma Kefi  1 , Fatima Jaziri  2 , Khaoula Ben Abdelghani  1 , Sami Turki  1
Affiliations
Case Reports

Early onset of scleromyxedema Arndt-Gottron associated with a monoclonal gammapathy: Successful treatment with intravenous immunoglobulins

Asma Kefi et al. Clin Case Rep. .

Abstract

Arndt-Gottron (S-AG) syndrome or scleromyxedema is a scarce disease characterized by a generalized papular and sclerodermoid eruption and systemic manifestations that can lead to significant morbid-mortality. Interesting, S-AG can be associated with a paraprotein. We report an exceptional scleromyxedema case associated with a benign monoclonal gammapathy in an old woman.

Keywords: Arndt‐Gottron syndrome; monoclonal gammapathy; scleromyxedema; treatment.

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Conflict of interest statement

The authors declare that they have no conflict of interest.

Figures

FIGURE 1
FIGURE 1
Reddened and indurated skin on the neck and on the upper trunk with eruption of lichenoid papules
FIGURE 2
FIGURE 2
Reddened and indurated skin on the neck with eruption of lichenoid papules
See this image and copyright information in PMC

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