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Review
. 2022 Jul 28:9:917973.
doi: 10.3389/fmed.2022.917973. eCollection 2022.

IPF Respiratory Symptoms Management - Current Evidence

Piotr Janowiak  1 , Amelia Szymanowska-Narloch  1 , Alicja Siemińska  1
Affiliations
Review

IPF Respiratory Symptoms Management - Current Evidence

Piotr Janowiak et al. Front Med (Lausanne). .

Abstract

Idiopathic pulmonary fibrosis (IPF) is a progressive, chronic disease of the lungs which is characterized by heavy symptom burden, especially in the last year of life. Despite recently established anti-fibrotic treatment IPF prognosis is one of the worst among interstitial lung diseases. In this review available evidence regarding pharmacological and non-pharmacological management of the main IPF symptoms, dyspnea and cough, is presented.

Keywords: ambulatory oxygen therapy (AOT); breathlessness; cough; dyspnea; high flow nasal cannula (HFNC); idiopathic pulmonary fibrosis (IPF); non-invasive positive pressure ventilation (NIPPV); non-invasive ventilation (NIV).

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Conflict of interest statement

The authors declare that the research was conducted in the absence of any commercial or financial relationships that could be construed as a potential conflict of interest.

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