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. 2023 Jan 15;207(2):211-214.
doi: 10.1164/rccm.202208-1470LE.

Progressive Interstitial Lung Disease in Relatives of Patients with Pulmonary Fibrosis

Jonathan A Rose  1 , Maria A Planchart Ferretto  1 , Anthony H Maeda  1 , Maria F Perez Garcia  2 , Nikkola E Carmichael  3 , Swati Gulati  1 , Mary B Rice  4 , Hilary J Goldberg  1 , Rachel K Putman  1 , Hiroto Hatabu  5 , Benjamin A Raby  3 , Ivan O Rosas  2 , Gary M Hunninghake  1
Affiliations

Progressive Interstitial Lung Disease in Relatives of Patients with Pulmonary Fibrosis

Jonathan A Rose et al. Am J Respir Crit Care Med. .
No abstract available

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Figures

Figure 1.
Figure 1.
Computed tomography scans of the chest from two relatives with interstitial lung abnormalities (ILA) and progression at the 2-year follow-up. The first participant with ILA at baseline and 2-year follow-up had radiologic progression, including worsening reticulations throughout the lungs (white arrows) and increased basilar traction bronchiolectasis (black arrow). At the 2-year follow-up, FVC had decreased by 7% and DlCO by 17%. The second participant was indeterminate for ILA at baseline but had ILA at the 2-year follow-up and radiologic progression, including new and increased areas of upper lobe and basilar reticulation (white arrows) as well as new basilar traction bronchiolectasis (black arrow). At the 2-year follow-up, FVC had decreased by 15% and DlCO by 16%.
See this image and copyright information in PMC

References

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