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Case Reports
. 2022 Jun 30;33(2):256-258.
doi: 10.31138/mjr.33.2.256. eCollection 2022 Jun.

Erythromelalgia in an Adolescent Female

Eleftheria Mamatsi  1 , Melpomeni Giorgi  1 , Argirios Dinopoulos  1 , Vasiliki Papaevangelou  1 , Lampros Fotis  1
Affiliations
Case Reports

Erythromelalgia in an Adolescent Female

Eleftheria Mamatsi et al. Mediterr J Rheumatol. .

Abstract

Erythromelalgia is a disabling syndrome of paroxysmal vasodilation affecting the feet, hands and face characterised by patient's cooling behaviour to achieve symptom relief. It can be primary or secondary and although a rare disorder it has been described in children and adolescents. We describe the case of a 14-year-old female diagnosed with primary erythromelalgia successfully treated with aspirin, amitriptyline, and carbamazepine.

Keywords: amitriptyline; aspirin; carbamazepine; child; erythromelalgia.

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Conflict of interest statement

The authors declare no conflict of interest.

Figures

Figure 1.
Figure 1.
Redness and oedema of fingers and dorsal hands.
Figure 2.
Figure 2.
Maceration of the skin of the palm.
Figure 3.
Figure 3.
Dorsal hands 15 days after treatment initiation.
Figure 4.
Figure 4.
Normal palm skin 15 days after treatment initiation.
See this image and copyright information in PMC

References

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