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Review
. 2023 Jan;44(1):15-23.
doi: 10.1007/s00246-022-03011-x. Epub 2022 Sep 23.

Multimodality Imaging in Ebstein Anomaly

Tarek Alsaied  1 , Adam B Christopher  2 , Jose Da Silva  3   4 , Aditi Gupta  2 , Victor O Morell  3   4 , Lizabeth Lanford  2 , Jacqueline G Weinberg  2 , Brian Feingold  2 , Thomas Seery  2 , Arvind Hoskoppal  2 , Bryan H Goldstein  2 , Jennifer A Johnson  2 , Laura J Olivieri  2 , Luciana De Fonseca Da Silva  3   4
Affiliations
Review

Multimodality Imaging in Ebstein Anomaly

Tarek Alsaied et al. Pediatr Cardiol. 2023 Jan.

Abstract

Ebstein anomaly is the most common form of tricuspid valve congenital anomalies. The tricuspid valve is abnormal with different degrees of displacement of the septal leaflet and abnormal rotation of the valve towards the right ventricular outflow tract. In severe forms, it results in significant tricuspid regurgitation and requires surgical repair. There is an increased interest in understanding the anatomy of the tricuspid valve in this lesion as the surgical repair has evolved with the invention and wide adoption of the cone operation. Multimodality imaging plays an important role in diagnosis, follow-up, surgical planning and post-operative care. This review provides anatomical tips for the cardiac imagers caring for patients with Ebstein anomaly and will help provide image-based personalized medicine.

Keywords: Adults with congenital heart disease; Cardiac MRI; Congenital heart disease; Ebstein; Tricuspid valve.

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References

    1. Barbara DW, Edwards WD, Connolly HM, Dearani JA (2008) Surgical pathology of 104 tricuspid valves (2000–2005) with classic right-sided Ebstein’s malformation. Cardiovasc Pathol 17(3):166–171 - DOI
    1. Dearani JA (2020) Ebstein repair: how I do it. JTCVS Tech 3:269–276 - DOI
    1. Lange R, Burri M, Eschenbach LK, Badiu CC, da Silva JP, Nagdyman N et al (2015) Da Silva's cone repair for Ebstein's anomaly: effect on right ventricular size and function. Eur J Cardiothorac Surg 48(2):316–320; discussion 20–21
    1. Lianza AC, Rodrigues ACT, Mercer-Rosa L, Vieira MLC, de Oliveira WAA, Afonso TR et al (2020) Right ventricular systolic function after the cone procedure for Ebstein’s anomaly: comparison between echocardiography and cardiac magnetic resonance. Pediatr Cardiol 41(5):985–995 - DOI
    1. da Silva JP, Baumgratz JF, da Fonseca L, Franchi SM, Lopes LM, Tavares GM et al (2007) The cone reconstruction of the tricuspid valve in Ebstein’s anomaly. The operation: early and midterm results. J Thorac Cardiovasc Surg 133(1):215–223 - DOI

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