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Review
. 2022 Jun 23:42:147.
doi: 10.11604/pamj.2022.42.147.29078. eCollection 2022.

Peri-orbital Masson's tumor: a case report and literature review

Lamia Benantar  1 , Sarah Belghmaidi  2 , El Mehdi Hamidi  1 , Yassine Ait M'barek  1 , Yassine El Ghani  2 , Ibtissam Hajji  2 , Abdeljalil Moutaouakil  2 , Khalid Aniba  1
Affiliations
Review

Peri-orbital Masson's tumor: a case report and literature review

Lamia Benantar et al. Pan Afr Med J. .

Abstract

Masson tumor is a benign vascular lesion characterized by an intravascular papillary endothelial hyperplasia. Peri orbital locations are rare. We report a case of Masson tumor localized in the upper internal angle of the left orbit revealed by progressive ocular proptosis. Orbital computed tomography (CT) scan and magnetic resonance imaging (MRI) showed a vascular mass in the left internal canthus mimicking an arterioveinous malformation. The patient underwent total removal of the lesion with a favorable postoperative follow up. Histological examination found an intravascular papillary endothelial hyperplasia without atypical features corresponding to Masson tumor. A thorough literature review of Masson tumor is presented with a discussion of clinical findings and management.

Keywords: Masson tumor; case report; intravascular papillary endothelial hyperplasia; management; orbital.

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Conflict of interest statement

The authors declare no competing interests.

Figures

Figure 1
Figure 1
(A,B) clinical examination showing impairment and varix of upper left eyelid
Figure 2
Figure 2
pre-operative clinical examination showing mildly restricted ocular motility
Figure 3
Figure 3
orbital CT scan with enhancement: (A,B) axial section; (C,D) coronal section, showing vascular lesion of the upper internal angle of left orbit
Figure 4
Figure 4
(A) orbito encephalic MRI; (B) axial and coronal T1 section: image of orbital mass in upper internal angle of left orbit, the lesion has an in heterogeneous hypersignal with serpiginous appearance; (C) axial T1 section with gadolinium enhancement, the mass has intense contrast enhancement; (D, E, F) axial and coronal T2 section, axial diffusion section: heterogeneous hypersignal lesion with serpiginous appearance mimicking an arteriovenous malformation
Figure 5
Figure 5
(A,B) histological examination finding endothelial cells with solid area of fibrosis and papillary hyperplasia limited to vascular wall without atypical features
See this image and copyright information in PMC

References

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