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. 2021 Oct 1;5(2):V14.
doi: 10.3171/2021.7.FOCVID21122. eCollection 2021 Oct.

Translabyrinthine resection of NF2 associated vestibular schwannoma with cochlear implant insertion

Cathal John Hannan  1   2 , Priya Sharma  3 , Matthew Edward Smith  4   5 , Laurence Johann Glancz  1 , Martin O'Driscoll  6 , Andrew Thomas King  1   2   7 , Charlotte Hammerbeck-Ward  1 , Dafydd Gareth Evans  8   9 , Scott Alexander Rutherford  1 , Simon Kinsella Lloyd  4   5   10 , Simon Richard Mackenzie Freeman  4   5 , Omar Nathan Pathmanaban  1   2   10
Affiliations

Translabyrinthine resection of NF2 associated vestibular schwannoma with cochlear implant insertion

Cathal John Hannan et al. Neurosurg Focus Video. .

Abstract

The authors present the case of a 24-year-old female with neurofibromatosis type 2. Growth of the left vestibular schwannoma and progressive hearing loss prompted the decision to proceed to translabyrinthine resection with cochlear nerve preservation and cochlear implant insertion. Complete resection with preservation of the facial and cochlear nerves was achieved. The patient had grade 1 facial function and was discharged on postoperative day 4 following suturing of a minor CSF leak. This case highlights the feasibility of cochlear nerve preservation and cochlear implant insertion in appropriately selected patients, offering a combination of effective tumor control and hearing rehabilitation. The video can be found here: https://stream.cadmore.media/r10.3171/2021.7.FOCVID21122.

Keywords: hearing rehabilitation; neurofibromatosis type 2; vestibular schwannoma.

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Conflict of interest statement

Disclosures Dr. Evans reports personal fees from AstraZeneca, outside the submitted work.Dr. Evans reports personal fees from AstraZeneca, outside the submitted work.

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