Clinical and pathological features of cutaneous manifestations in VEXAS syndrome: A multicenter retrospective study of 59 cases

Ève Zakine¹, Loula Papageorgiou², Rim Bourguiba³, Arsène Mekinian⁴, Benjamin Terrier⁵, Olivier Kosmider⁶, Pierre Hirsch², Marie Jachiet¹, Sylvain Audia⁷, Samuel Ardois⁸, Léopold Adélaïde⁹, Adrien Bigot¹⁰, Paul Duriez¹¹, Jean-François Emile¹², Estibaliz Lazaro¹³, Damien Fayard¹⁴, Joris Galland¹⁵, Miguel Hié¹⁶, Sébastien Humbert¹⁷, Alexis Jean¹³, Marie Kostine¹⁸, Valentin Lacombe¹⁹, Guillaume Le Guenno²⁰, Hervé Lobbes²⁰, Nadine Magy-Bertrand¹⁷, Paola Marianetti-Guingel²¹, Alexis Mathian¹⁶, Rodérau Outh²², Clémence Saillard²³, Maxime Samson⁷, Guillaume Vial¹³, Jean-David Bouaziz¹, Philippe Moguelet²⁴, François Chasset²⁵; National French VEXAS Study Group (NFVS)

Collaborators, Affiliations

Collaborators

National French VEXAS Study Group (NFVS):
Z Amoura, A Aouba, C Arnaud, A Audemard-Verger, C Bachmeyer, B Bienvenu, P Biscay, F Borlot, L Bouillet, G Boursier, F Carrat, T Cluzeau, T Comont, A Constantin, B de Sainte Marie, C Deligny, C Dieval, E Duroyon, M Ebbo, O Fain, B Faucher, P Fenaux, S Georgin-Lavialle, M Gerfaud-Valentin, J Graveleau, A F Guedon, T Hanslik, M Heiblig, V Jachiet, Y Jamilloux, J Jeannel, M Larue, F Le Pelletier, E Liozon, A Meyer, T Moulinet, M Pha, J Rossignol, M Roux, M Roux-Sauvat, L Sailler, G Sarrabay, M Sebert, A Servettaz, P Sujobert, L Terriou, J Vinit, S Vinzio, T Weitten, L P Zhao

Affiliations

¹ Dermatology Department, Paris University, Faculty of Medicine, AP-HP, Saint Louis University Hospital, Paris, France.
² Hematology and Cytology Department, Sorbonne University, INSERM, Saint Antoine Research Center, AP-HP, Saint Antoine University Hospital, Paris, France.
³ Internal Medicine Department, Sorbonne University, Faculty of Medicine, AP-HP, Tenon University Hospital, Paris, France.
⁴ Internal Medicine Department, Sorbonne University, Faculty of Medicine, AP-HP, Saint Antoine University Hospital, Paris, France.
⁵ Internal Medicine Department, Paris University, Faculty of Medicine, AP-HP, Cochin University Hospital, Paris, France.
⁶ Hematology Department, Paris University, Faculty of Medicine, AP-HP, Cochin University Hospital, Paris, France.
⁷ Internal Medicine Department, Bourgogne University, Faculty of Medicine, Dijon University Hospital, Dijon, France.
⁸ Internal Medicine Department, Rennes University, Faculty of Medicine, Rennes University Hospital, Rennes, France.
⁹ Internal Medicine Department, Claude Bernard Lyon 1 University, Faculty of Medicine, Croix-Rousse Hospital, Lyon, France.
¹⁰ Internal Medicine Department, Tours University, Faculty of Medicine, Tours University Hospital, Tours, France.
¹¹ Pathology Department, Sorbonne University, Faculty of Medicine, AP-HP, Saint Antoine University Hospital, Paris, France.
¹² Pathology Department, Versailles Saint Quentin University, Faculty of Medicine, Ambroise Paré Hospital, Boulogne-Billancourt, France.
¹³ Internal Medicine Department, Bordeaux University, Faculty of Medicine, Bordeaux University Hospital, Bordeaux, France.
¹⁴ Internal Medicine Department, Clermont-Ferrand University, Faculty of Medicine, Gabriel Montpied University Hospital, Clermont-Ferrand, France.
¹⁵ Internal Medicine Department, Fleyriat Hospital, Bourg-en-Bresse, France.
¹⁶ Internal Medicine Department, Sorbonne University, Faculty of Medicine, AP-HP, Pitié-Salpêtrière University Hospital, Paris, France.
¹⁷ Internal Medicine Department, Besançon University, Faculty of Medicine, Besançon University Hospital, Paris, France.
¹⁸ Rheumatology Department, Bordeaux University, Faculty of Medicine, Bordeaux University Hospital, Bordeaux, France.
¹⁹ Internal Medicine Department, Clermont-Ferrand University, Faculty of Medicine, Estaing University Hospital, Clermont-Ferrand, France.
²⁰ Internal Medicine and Clinical Immunology Department, Angers University, Faculty of Medicine, Angers University Hospital, Angers, France.
²¹ Internal Medicine Department, Reims University, Faculty of Medicine, Reims University Hospital, Reims, France.
²² Internal Medicine Department, Perpignan Hospital Center, Perpignan, France.
²³ Dermatology Department, Rennes University, Faculty of Medicine, Rennes University Hospital, Rennes, France.
²⁴ Pathology Department, Sorbonne University, Faculty of Medicine, AP-HP, Tenon University Hospital, Paris, France.
²⁵ Dermatology and Allergology Department, Sorbonne University, Faculty of Medicine, AP-HP, Tenon University Hospital, Paris, France. Electronic address: francois.chasset@aphp.fr.

PMID: 36343774
DOI: 10.1016/j.jaad.2022.10.052

Multicenter Study

Clinical and pathological features of cutaneous manifestations in VEXAS syndrome: A multicenter retrospective study of 59 cases

Ève Zakine et al. J Am Acad Dermatol. 2023 Apr.

. 2023 Apr;88(4):917-920.

doi: 10.1016/j.jaad.2022.10.052. Epub 2022 Nov 5.

Authors

Collaborators

National French VEXAS Study Group (NFVS):
Z Amoura, A Aouba, C Arnaud, A Audemard-Verger, C Bachmeyer, B Bienvenu, P Biscay, F Borlot, L Bouillet, G Boursier, F Carrat, T Cluzeau, T Comont, A Constantin, B de Sainte Marie, C Deligny, C Dieval, E Duroyon, M Ebbo, O Fain, B Faucher, P Fenaux, S Georgin-Lavialle, M Gerfaud-Valentin, J Graveleau, A F Guedon, T Hanslik, M Heiblig, V Jachiet, Y Jamilloux, J Jeannel, M Larue, F Le Pelletier, E Liozon, A Meyer, T Moulinet, M Pha, J Rossignol, M Roux, M Roux-Sauvat, L Sailler, G Sarrabay, M Sebert, A Servettaz, P Sujobert, L Terriou, J Vinit, S Vinzio, T Weitten, L P Zhao

Affiliations

¹ Dermatology Department, Paris University, Faculty of Medicine, AP-HP, Saint Louis University Hospital, Paris, France.
² Hematology and Cytology Department, Sorbonne University, INSERM, Saint Antoine Research Center, AP-HP, Saint Antoine University Hospital, Paris, France.
³ Internal Medicine Department, Sorbonne University, Faculty of Medicine, AP-HP, Tenon University Hospital, Paris, France.
⁴ Internal Medicine Department, Sorbonne University, Faculty of Medicine, AP-HP, Saint Antoine University Hospital, Paris, France.
⁵ Internal Medicine Department, Paris University, Faculty of Medicine, AP-HP, Cochin University Hospital, Paris, France.
⁶ Hematology Department, Paris University, Faculty of Medicine, AP-HP, Cochin University Hospital, Paris, France.
⁷ Internal Medicine Department, Bourgogne University, Faculty of Medicine, Dijon University Hospital, Dijon, France.
⁸ Internal Medicine Department, Rennes University, Faculty of Medicine, Rennes University Hospital, Rennes, France.
⁹ Internal Medicine Department, Claude Bernard Lyon 1 University, Faculty of Medicine, Croix-Rousse Hospital, Lyon, France.
¹⁰ Internal Medicine Department, Tours University, Faculty of Medicine, Tours University Hospital, Tours, France.
¹¹ Pathology Department, Sorbonne University, Faculty of Medicine, AP-HP, Saint Antoine University Hospital, Paris, France.
¹² Pathology Department, Versailles Saint Quentin University, Faculty of Medicine, Ambroise Paré Hospital, Boulogne-Billancourt, France.
¹³ Internal Medicine Department, Bordeaux University, Faculty of Medicine, Bordeaux University Hospital, Bordeaux, France.
¹⁴ Internal Medicine Department, Clermont-Ferrand University, Faculty of Medicine, Gabriel Montpied University Hospital, Clermont-Ferrand, France.
¹⁵ Internal Medicine Department, Fleyriat Hospital, Bourg-en-Bresse, France.
¹⁶ Internal Medicine Department, Sorbonne University, Faculty of Medicine, AP-HP, Pitié-Salpêtrière University Hospital, Paris, France.
¹⁷ Internal Medicine Department, Besançon University, Faculty of Medicine, Besançon University Hospital, Paris, France.
¹⁸ Rheumatology Department, Bordeaux University, Faculty of Medicine, Bordeaux University Hospital, Bordeaux, France.
¹⁹ Internal Medicine Department, Clermont-Ferrand University, Faculty of Medicine, Estaing University Hospital, Clermont-Ferrand, France.
²⁰ Internal Medicine and Clinical Immunology Department, Angers University, Faculty of Medicine, Angers University Hospital, Angers, France.
²¹ Internal Medicine Department, Reims University, Faculty of Medicine, Reims University Hospital, Reims, France.
²² Internal Medicine Department, Perpignan Hospital Center, Perpignan, France.
²³ Dermatology Department, Rennes University, Faculty of Medicine, Rennes University Hospital, Rennes, France.
²⁴ Pathology Department, Sorbonne University, Faculty of Medicine, AP-HP, Tenon University Hospital, Paris, France.
²⁵ Dermatology and Allergology Department, Sorbonne University, Faculty of Medicine, AP-HP, Tenon University Hospital, Paris, France. Electronic address: francois.chasset@aphp.fr.

PMID: 36343774
DOI: 10.1016/j.jaad.2022.10.052

No abstract available

Keywords: Sweet's syndrome; VEXAS syndrome; dermatopathology; neutrophilic dermatoses.

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Conflicts of interest None disclosed.

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Clinical and pathological features of cutaneous manifestations in VEXAS syndrome: A multicenter retrospective study of 59 cases

Collaborators

Affiliations

Clinical and pathological features of cutaneous manifestations in VEXAS syndrome: A multicenter retrospective study of 59 cases

Authors

Collaborators

Affiliations

Conflict of interest statement

Publication types

MeSH terms

Supplementary concepts

LinkOut - more resources

Full Text Sources