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. 2022 Nov 7;11(21):6601.
doi: 10.3390/jcm11216601.

Surgical and Medical Aspects of the Initial Treatment of Biliary Atresia: Position Paper

Mark Davenport  1 , Omid Madadi-Sanjani  2 , Christophe Chardot  3 , Henkjan J Verkade  4 , Saul J Karpen  5 , Claus Petersen  2
Affiliations

Surgical and Medical Aspects of the Initial Treatment of Biliary Atresia: Position Paper

Mark Davenport et al. J Clin Med. .

Abstract

Biliary atresia, a fibro-obliterative disease of the newborn, is usually initially treated by Kasai portoenterostomy, although there are many variations in technique and different options for post-operative adjuvant medical therapy. A questionnaire on such topics (e.g., open vs. laparoscopic; the need for liver mobilisation; use of post-operative steroids; use of post-operative anti-viral therapy, etc.) was circulated to delegates (n = 43) of an international webinar (Biliary Atresia and Related Diseases-BARD) held in June 2021. Respondents were mostly European, but included some from North America, and represented 18 different countries overall. The results of this survey are presented here, together with a commentary and review from an expert panel convened for the meeting on current trends in practice.

Keywords: Kasai operation; adjuvant therapy; biliary atresia; corticosteroids; cytomegalovirus; ursodeoxycholic acid.

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Conflict of interest statement

The authors declare no conflict of interest.

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