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. 2022 Dec;12(6):e228-e231.
doi: 10.1212/CPJ.0000000000200088.

Intracranial Corkscrew Angiopathy

Rakhee Lalla  1 , Deepti Virmani  1 , Kushak Suchdev  1 , Crandall E Peeler  1 , Mohamad Abdalkader  1 , Thanh N Nguyen  1
Affiliations

Intracranial Corkscrew Angiopathy

Rakhee Lalla et al. Neurol Clin Pract. 2022 Dec.

Abstract

Objectives: The objective of this case report was to describe a rare presentation of corkscrew cerebral angiopathy presenting as subarachnoid hemorrhage (SAH).

Methods: We present a young woman who presented with a thunderclap headache, found to have a nonaneurysmal SAH.

Results: Cerebral angiogram revealed corkscrew angiopathy in medium-sized vessels and multiple micro-occlusions with collateralization. No intracranial aneurysm was detected. Extensive workup for vasculitis and genetic causes for vasculopathy was unrevealing. The patient had no neurologic deficits, and her symptoms resolved.

Discussion: This is an extremely rare presentation of subarachnoid hemorrhage due to corkscrew angiopathy.

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Figures

Figure 1
Figure 1. Noncontrast CT Showing Acute SAH Within the Left Sylvian Fissure
SAH = subarachnoid hemorrhage.
Figure 2
Figure 2. CT Angiogram Showing Suspected Bilobed Left M2 Aneurysm
Figure 3
Figure 3. Lateral View of the Left ICA Showing Multifocal Corkscrew Appearance of the Left MCA and ACA Branches
The left ophthalmic artery is absent. ACA = anterior cerebral artery; ICA = internal cerebral artery; MCA = middle cerebral artery.
Figure 4
Figure 4. Right-Eye Fundus Photograph Demonstrating Retinal Arteriolar Tortuosity With Normal Venuoles
See this image and copyright information in PMC

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