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Case Reports
. 2022 Nov 17:84:104926.
doi: 10.1016/j.amsu.2022.104926. eCollection 2022 Dec.

Congenital megalourethra

Turyalai Hakimi  1
Affiliations
Case Reports

Congenital megalourethra

Turyalai Hakimi. Ann Med Surg (Lond). .

Abstract

Background: Congenital megalourethra is a urogenital anomaly characterized by a cystic dilatation and elongation of the penile urethra resulting from the absence and hypoplasia of the corpus spongiosum and corpus cavernosum, or anterior urethral valve. There are two clinical types: scaphoid and fusiform. Generally, the etiology is unknown, but it is thought to be a defect in mesodermal development. Fewer than 100 cases have been reported in the literature, and the exact incidence is unclear. In most cases, the surgical procedure is challenging and requires extensive reconstructive and/or replacement surgery.

Case presentation: We present a 6-month-old boy suffering from a cystic dilatation of the penile urethra along with urine dribbling during micturition since birth. The patient was diagnosed with the scaphoid type of megalourethra and was operated on using reduction urethroplasty. On the 21st post-operative day, we removed the Foley catheter and followed the patient on two occasions (the 45th post-operative day and the 6th post-operative month) with excellent results.

Conclusion: The anagement of megalourethra depends on the clinical type. Meticulous surgical technique, the use of fine suture materials with careful handling, and fixation of the vascularized flap are the main principles of an acceptable result. Observation of erectile function and fertility require long-term follow-up.

Keywords: Case report; Fusiform; Megalourethra; Scaphoid; Urethroplasty.

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Conflict of interest statement

The author declares that he has no known competing financial interests or personal relationships that could have appeared to influence the work reported in this paper.

Figures

Fig. 1
Fig. 1
Excessive dilation of penile urethra filled with urine.
Fig. 2
Fig. 2
(A). Open dilated urethra following urethral midline incision with silicon catheter in place, (B). Two-layer urethroplasty, (C). Vascularized subdartos flap fixation over the urethroplasty. (For interpretation of the references to colour in this figure legend, the reader is referred to the Web version of this article.)
Fig. 3
Fig. 3
A&B Represent normal voiding and acceptable cosmetic penile appearance.
See this image and copyright information in PMC

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