Preventing Continuous Damage in Primary Ciliary Dyskinesia: Is Airway Inflammation a Potential Target?
- PMID: 36584988
- PMCID: PMC9819273
- DOI: 10.1513/AnnalsATS.202209-782ED
Preventing Continuous Damage in Primary Ciliary Dyskinesia: Is Airway Inflammation a Potential Target?
Comment on
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Airway Inflammation in Children with Primary Ciliary Dyskinesia.Ann Am Thorac Soc. 2023 Jan;20(1):67-74. doi: 10.1513/AnnalsATS.202204-314OC. Ann Am Thorac Soc. 2023. PMID: 35984413 Free PMC article.
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- Shapiro AJ, Zariwala MA, Ferkol T, Davis SD, Sagel SD, Dell SD, et al. Genetic Disorders of Mucociliary Clearance Consortium Diagnosis, monitoring, and treatment of primary ciliary dyskinesia: PCD Foundation consensus recommendations based on state of the art review. Pediatr Pulmonol . 2016;51:115–132. - PMC - PubMed
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- Ratjen F, Waters V, Klingel M, McDonald N, Dell S, Leahy TR, et al. Changes in airway inflammation during pulmonary exacerbations in patients with cystic fibrosis and primary ciliary dyskinesia. Eur Respir J . 2016;47:829–836. - PubMed
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- Bush A, Payne D, Pike S, Jenkins G, Henke MO, Rubin BK. Mucus properties in children with primary ciliary dyskinesia: comparison with cystic fibrosis. Chest . 2006;129:118–123. - PubMed
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