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Case Reports
. 2023 Jan 7;18(3):1121-1126.
doi: 10.1016/j.radcr.2022.12.046. eCollection 2023 Mar.

Multiple system atrophy-cerebellar: A case report and literature review

Thi Thuong Doan  1 , Thuy Dung Pham  1 , Duy Duan Nguyen  2 , Dac Hong An Ngo  1 , Trong Binh Le  1 , Thanh Thao Nguyen  1
Affiliations
Case Reports

Multiple system atrophy-cerebellar: A case report and literature review

Thi Thuong Doan et al. Radiol Case Rep. .

Abstract

We reported a case of a 48-year-old female patient admitted to the hospital due to balance disorder which progressed rapidly within 1 week. Cerebral magnetic resonance imaging showed significant atrophy and hyperintensities at the middle cerebellar peduncles and the "hot cross bun" sign of the pons. The final diagnosis was probable multiple system atrophy, cerebellar subtype. The clinical and imaging findings will be discussed as well as a brief literature review.

Keywords: MRI; Multiple system atrophy; Neuroradiology.

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Figures

Fig 1
Fig. 1
Axial T2-weighted images showed “hot cross bun” sign of the pon (arrows).
Fig 2
Fig. 2
Axial FLAIR (left) and T2-weighted images (right) showed symmetric atrophy of middle cerebellar peduncles with hyperintensities (arrows).
Fig 3
Fig. 3
Axial T2-weighted image showed no abnormalities in the basal ganglia.
Fig 4
Fig. 4
Maximum intensity projection (MIP) reconstruction in axial (left) and coronal (right) planes of time-of-flight (TOF) sequence of cerebral arteries showed no abnormalities.
See this image and copyright information in PMC

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