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Case Reports
. 2023 Jan 20;10(1):2158833.
doi: 10.1080/23320885.2022.2158833. eCollection 2023.

Atypical presentation of forearm compartment syndrome in a case of vascular type Ehlers-Danlos syndrome

Tsang Yeung  1 , Ching San Esther Chow  1
Affiliations
Case Reports

Atypical presentation of forearm compartment syndrome in a case of vascular type Ehlers-Danlos syndrome

Tsang Yeung et al. Case Reports Plast Surg Hand Surg. .

Abstract

A 30-year-old Chinese man with vascular type Ehlers-Danlos Syndrome presents with spontaneous right forearm compartment syndrome due to pseudoaneurysms along the radial artery. Emergency fasciotomy and reconstruction of the radial artery with a saphenous vein graft were performed. Genetic test showed a heterozygous DNA change c. 1852 G > C in COL3A1 gene.

Keywords: Compartment syndrome; Ehlers–Danlos syndrome; Hong Kong Chinese; pseudoaneurysm; saphenous vein graft.

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Conflict of interest statement

Pre-amended version of this manuscript HAS been wrongly submitted for publication to a predatory journal, namely ‘Journals of Clinical Orthopaedics and Trauma Care’ under ‘Auctores Publishing LLC’ but have been removed. Here I attach the confirmation e-mail from Auctores:

Figures

Figure 1.
Figure 1.
Clinical Photo of patient on admission. There was marked swelling, bruising over bilateral forearms.
Figure 2.
Figure 2.
CT Angiogram showed multiple pseudoaneurysms along radial and ulnar arteries.
Figure 3.
Figure 3.
15 cm segment of the radial artery was found to be thinned-wall and friable, with multiple sites of rupture (Blue arrows).
Figure 4.
Figure 4.
Saphenous vein graft was harvest from left medial thigh.
Figure 5.
Figure 5.
The vein graft was used to reconstruct the vascular defect (Yellow segment).
Figure 6.
Figure 6.
Clinical Photo of patient’s right forearm after skin grafting.
Figure 7.
Figure 7.
Four years after operation – the skin graft incorporated and the wound healed well.
See this image and copyright information in PMC

References

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