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Case Reports
. 2022 Dec 31;14(12):e33170.
doi: 10.7759/cureus.33170. eCollection 2022 Dec.

Jaccoud's Arthropathy in a Case of Mixed Connective Tissue Disorder: An Interesting Tale

Jahnabi Bhagawati  1 , Mansi Patel  1 , Keyur Saboo  2 , Sunil Kumar  1 , Sourya Acharya  1
Affiliations
Case Reports

Jaccoud's Arthropathy in a Case of Mixed Connective Tissue Disorder: An Interesting Tale

Jahnabi Bhagawati et al. Cureus. .

Abstract

In Jaccoud's arthropathy (JA), classical deformities that resemble rheumatoid arthritis (RA), such as swan neck deformity and ulnar deviation, are present, but in contrast to RA, these are reducible to passive movement and nonerosive arthritis. Similar deformities are also described in various connective tissue disorders. Mixed connective tissue disease (MCTD) characteristically has overlapping features of various connective tissue diseases (CTDs) such as systemic lupus erythematosus, systemic sclerosis, and myosotis with an association of U1RNP antibody. Approximately 60% of patients with MCTD may have deforming arthritis. We present a case of a 23-year-old male, with multiple overlapping clinical features and deforming arthritis. This case begs the question to identify various possible differentials of deforming arthritis.

Keywords: hand deformities; interstitial lung disease; jaccoud’s arthropathy; mixed connective tissue disease; rheumatoid like.

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Conflict of interest statement

The authors have declared that no competing interests exist.

Figures

Figure 1
Figure 1. Jaccoud's arthropathy.
Figure 2
Figure 2. HRCT thorax revealed ground glass opacity.
HRCT, high-resolution computed tomography
Figure 3
Figure 3. X-ray revealing nonerosive deformity.
Figure 4
Figure 4. Nailfold capillaroscopy showing dilated capillaries.
See this image and copyright information in PMC

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