Skip to main page content
U.S. flag

An official website of the United States government

Dot gov

The .gov means it’s official.
Federal government websites often end in .gov or .mil. Before sharing sensitive information, make sure you’re on a federal government site.

Https

The site is secure.
The https:// ensures that you are connecting to the official website and that any information you provide is encrypted and transmitted securely.

Access keys NCBI Homepage MyNCBI Homepage Main Content Main Navigation
. 2023 May 1;34(3):e330-e331.
doi: 10.1097/SCS.0000000000009259. Epub 2023 Mar 13.

Worth Syndrome-Patient Report, Diagnostic Work-Up, and Surgical Management of a Rare Craniofacial Entity

Mark S Shafarenko  1 , Hagen B Klieb  2 , Oleh M Antonyshyn  1   3
Affiliations

Worth Syndrome-Patient Report, Diagnostic Work-Up, and Surgical Management of a Rare Craniofacial Entity

Mark S Shafarenko et al. J Craniofac Surg. .

Abstract

Worth syndrome is a rare genetic bone disorder that often presents with cortical thickening of the mandible and an increase in mandibular width. The authors report the preoperative considerations in a young female with Worth syndrome, operative planning, and successful mandibular reduction using cutting guides.

PubMed Disclaimer

Conflict of interest statement

The authors report no conflicts of interest.

References

    1. Merenzon MA, Dorman MA, Zuliani Sampaolesi P, et al. Case report of worth syndrome and Chiari I malformation: unusual association and surgical treatment. World Neurosurg 2018;115:225–228
    1. Payne K, Dickenson A. Worth syndrome as a diagnosis for mandibular osteosclerosis. Dentomaxillofac Radiol 2011;40:531–533
    1. Thompson KS, Owosho AA. Worth syndrome “mandibular osteosclerosis” as an incidental finding: a report of 2 cases. Dentomaxillofac Radiol 2018;47:20180171
    1. Gorlin R, Glass L. Autosomal dominant osteosclerosis. Radiology 1977;125:547–548
    1. Worth HM, Wollin D. Hyperostosis corticalis generalisata congenita. J Can Assoc Radiol 1966;17:67–74

Supplementary concepts

LinkOut - more resources