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. 2023 Dec;76(12):961-969.
doi: 10.1016/j.rec.2023.03.004. Epub 2023 Mar 15.

Characteristics and outcomes of the Spanish registry for pediatric patients with bicuspid aortic valve (REVAB)

[Article in English, Spanish]
Carolina Juzga-Corrales  1 , Ariadna Ayerza-Casas  2 , Marc Figueras-Coll  3 , Silvia Escribà-Bori  4 , Beatriz Plata-Izquierdo  5 , Rosa Collell  6 , María Arántzazu González-Marín  7 , José Manuel Siurana  8 , Moisés Sorlí  9 , Leticia Albert de la Torre  10 , Silvia Teodoro-Marín  11 , Mónica Rodríguez  12 , Olga Domínguez-García  13 , Sara Rellán  14 , Begoña Manso  15 , Bernardo López-Abel  16 , Roser Álvarez-Pérez  17 , Manuel Portillo-Márquez  18 , Erika Rezola  19 , Fernando Centeno-Malfaz  20 , Ruth Solana-Gracia  21 , Henar Rojo-Sombrero  22 , María Teresa Cantero-Tejedor  23 , Bibiana Riaño  24 , María Ángeles Tejero-Hernández  25 , Marisol Jiménez-Casso  26 , Ana María Pérez-Pardo  27 , Ana Moriano-Gutiérrez  28 , Manuel Marrero-Calvo  29 , María Teresa Fernández  30 , Carlos Salido-Peracaula  31 , María José Bravo  32 , Federico Gutiérrez-Larraya  33 , Anna Sabaté-Rotés  34
Affiliations

Characteristics and outcomes of the Spanish registry for pediatric patients with bicuspid aortic valve (REVAB)

[Article in English, Spanish]
Carolina Juzga-Corrales et al. Rev Esp Cardiol (Engl Ed). 2023 Dec.

Abstract

Introduction and objectives: Bicuspid aortic valve (BAV) disorder is the most common congenital heart disease. The aim of this study was to describe the characteristics of 0- to 18-year olds with BAV in a population-based registry.

Methods: Data from all pediatric patients were obtained from the Spanish registry for pediatric patients with bicuspid aortic valve (REVAB) (< 18 years). For data analysis, patients with BAV were divided into 2 groups by their features: isolated BAV and BAV with associated congenital heart disease.

Results: We included 1681 patients from 33 hospitals. Males accounted for 69.6% (n = 1158). Valve morphology was horizontal in 63.4% (n = 1012) and pure (Sievers type 0) in 28.4% (n=469). Isolated BAV was present in 63.7% (n=1060), and concomitant left-sided obstructive lesions in 23.4% (n=390). Interventions were required in 8.6% (n=145).

Conclusion: These data represent the first large, population-based description of the clinical presentations and outcomes of patients enrolled in the Spanish registry for pediatric patients with bicuspid aortic valve.

Keywords: Aorta; Bicuspid aortic valve; Válvula aórtica bicúspide.

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