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. 2023 Mar 3:11:1117060.
doi: 10.3389/fped.2023.1117060. eCollection 2023.

The relation between radiographic manifestation and clinical characteristics of congenital radioulnar synostosis in children: A retrospective study from multiple centers

Pan Hong  1 , Wei Tan  2 , Wei-Zheng Zhou  3 , Yu Zheng  4 , Jin Li  1 , PengFei Zheng  5 , Xin Tang  1
Affiliations

The relation between radiographic manifestation and clinical characteristics of congenital radioulnar synostosis in children: A retrospective study from multiple centers

Pan Hong et al. Front Pediatr. .

Abstract

Objective: To review the radiographic manifestation and clinical appearance of children with congenital radioulnar synostosis (CRUS) retrospectively.

Study design: Retrospective cohort study of children with CRUS from multiple medical centers.

Results: A total of 329 patients (male 259, female 70) with an average age of 5.4 years (0.5-16 years old), were included in this study. In particular, 145 patients (145/329, 44.1%) demonstrated bilateral involvement, and 184 patients (left 123, right 61) demonstrated unilateral involvement. As for Clear and Omery (C&O) classification, most patients belonged to Type III, and then followed by Type IV. As for Chinese Multi-center Pediatric Orthopedic Study Group (CMPOS) classification, most patients belonged to Type III, and then followed by Type II and Type I. In C&O Type III, 92.03% patients demonstrated severe pronation. According to CMPOS classification, 92.98% Type I patients demonstrated neutral to mild pronation, 72.17% Type II patients demonstrated moderate pronation, and 92.03% Type III patients demonstrated severe pronation. The age distribution showed no significant difference between C&O Type II and IV (P = 0.96); the pronation ankylosis severity showed no significant difference between C&O Type II and IV (P = 0.387).

Conclusion: Although CRUS is a rare forearm deformity, there are certain relation between radiographic manifestation and clinical forearm functional restriction. CRUS patients of C&O or CMPOS Type III classification might suffer severe pronation deformity and warrant early intervention.

Keywords: ankylosis; classification; congenital radioulnar synostosis; pronation; radiographic manifestation.

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Conflict of interest statement

The authors declare that the research was conducted in the absence of any commercial or financial relationships that could be construed as a potential conflict of interest.

Figures

Figure 1
Figure 1
X-ray or CT reconstruction of forearm deformities. (A) C & O Type I; CMPOS Type I. (B) C & O Type II; CMPOS Type II. (C) C & O Type III; CMPOS Type III. (D) C & O Type IV; CMPOS Type II.
See this image and copyright information in PMC

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