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. 2022 Dec 26;16(1):182-184.
doi: 10.4103/ojo.ojo_218_21. eCollection 2023 Jan-Apr.

A comprehensive ocular profile using multimodal imaging systems and surgical outcome in a patient with Alport syndrome

Soumen Sadhu  1 , Janarthanam Jothi Balaji  1 , Bhaskar Srinivasan  2
Affiliations

A comprehensive ocular profile using multimodal imaging systems and surgical outcome in a patient with Alport syndrome

Soumen Sadhu et al. Oman J Ophthalmol. .
No abstract available

Keywords: Aberrations; Alport syndrome; aberrometry; anterior lenticonus; lenticular myopia.

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Conflict of interest statement

There are no conflicts of interest.

Figures

Figure 1:
Figure 1:
Slit-lamp photograph of the left (a) and the right (b) eye shows the conical slit section of the protruding anterior capsule in the pupillary area, and the corresponding ASOCT image (c and d) showing the anterior cone of the lens with some underlying haze
Figure 2:
Figure 2:
Spectral domain optical coherence tomography (Carl Zeiss Cirrus 5000) showing a lateral view through the macula revealing temporal retinal thinning with foveal hypoplasia (OD: inner temporal retina: 258 μm; OS: inner temporal retina: 352 μm; outer temporal retina: 344 μm)
Figure 3:
Figure 3:
Oil droplet sign is intraoperatively seen in retroillumination (a), and redundancy of anterior capsule seep before capsulorhexis (b)
Figure 4:
Figure 4:
Preoperative ray-tracing wavefront aberrometry of the right eye (a) and the left eye (c) revealed increased defocus and negative spherical aberration, DLI of -0.10 along with the corresponding simulated Snellen's visual acuity. Significant decrease in all internal higher-order aberrations, total higher-order aberration, and improvement in DLI was noticed postoperatively in the right (b) and left eye (d). Note the improvement in simulated Snellen's visual acuity. DLI: Dysfunctional lens Index
See this image and copyright information in PMC

References

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