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Case Reports
. 2023 Mar 16;15(3):e36220.
doi: 10.7759/cureus.36220. eCollection 2023 Mar.

A Rare Presentation of Zinner Syndrome

Shayan Mahapatra  1 , Hovra Zahoor  2 , Abraham M Quader  3 , Jodi-Ann Chin  1
Affiliations
Case Reports

A Rare Presentation of Zinner Syndrome

Shayan Mahapatra et al. Cureus. .

Abstract

Zinner syndrome is a rare developmental anomaly of the distal Wolffian duct. It is characterized by a triad of unilateral renal agenesis, cysts in the ipsilateral seminal vesicle, and ipsilateral obstruction of the ejaculatory duct. While some patients are asymptomatic and diagnosed incidentally, other patients may present with symptoms related to obstructed ejaculatory ducts and seminal vesicle cysts. We report a unique case of a 32-year-old male who presented with pelvic pain for three days.

Keywords: developmental anomaly; ejaculatory disorders; renal agenesis; seminal vesical cyst; zinner’s syndrome.

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Conflict of interest statement

The authors have declared that no competing interests exist.

Figures

Figure 1
Figure 1. (A) Axial CT imaging with left renal agenesis. (B) Coronal CT imaging with left renal agenesis.
Figure 2
Figure 2. (A, B) MRI abdomen/pelvis revealed multiple cystic hyperintense structures in the region of the right seminal vesicle near the bladder base.
Figure 3
Figure 3. (A, B) Trans-rectal ultrasound image showing cystic structure in the seminal vesicle region.
See this image and copyright information in PMC

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