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Case Reports
. 2023 Apr 7:43:101843.
doi: 10.1016/j.rmcr.2023.101843. eCollection 2023.

A recurrent pleuropneumonia revealing Erdheim-Chester Disease

Yousra Kherabi  1 , Thibaud Chazal  2 , Jean-François Emile  3 , Wassim Allaham  4 , Elise Mallart  1 , Victoire de Lastours  1   5 , Julien Haroche  2 , Yann Nguyen  1
Affiliations
Case Reports

A recurrent pleuropneumonia revealing Erdheim-Chester Disease

Yousra Kherabi et al. Respir Med Case Rep. .

Abstract

Erdheim-Chester disease (ECD) is a rare form of L group histiocytosis, accounting for up to 1500 cases to date worldwide, which mainly affects men between their 5th and 7th decade of life. The most frequent manifestations are bone involvement, perirenal infiltration with an evocating appearance of "hairy kidneys", and a "coated aorta" aspect. Lung involvement in ECD is less common and includes pleural infiltration and interstitial lung disease. Herein, we report the case of a 76-year-old woman with recurrent pleuropneumonia revealing ECD.

Keywords: Erdheim-Chester; Histiocytosis; Pleuropneumonia.

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Conflict of interest statement

None.

Figures

Fig. 1
Fig. 1
A. Computed tomodensitometry showing a thickening of the right basal parietal pleura. B. Computed tomodensitometry showing a perivascular aortic infiltration. C. Abdominal computed tomodensitometry showing a perivascular aortic infiltration (“coated aorta” aspect) and a peri-renal infiltration (“hairy kidneys” aspect). D. Cardiac magnetic resonance imaging showing a pseudo-tumoral infiltration of atrioventricular groove and a right pleural effusion.
See this image and copyright information in PMC

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