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. 2023 Apr 26;25(Suppl C):C169-C172.
doi: 10.1093/eurheartjsupp/suad019. eCollection 2023 May.

Electrocardiogram in arrhytmogenic cardiomyopathy

Leonardo Calò  1 , Giada Oliviero  1 , Cinzia Crescenzi  1 , Fabiana Romeo  1 , Annamaria Martino  1 , Edoardo Bressi  1 , Matteo Stefanini  2 , Elisa Silvetti  1 , Ludovica Danza  1 , Marco Rebecchi  1 , Stefano Canestrelli  1 , Elisa Fedele  1 , Chiara Lanzillo  1 , Armando Fusco  2 , Ermenegildo De Ruvo  1
Affiliations

Electrocardiogram in arrhytmogenic cardiomyopathy

Leonardo Calò et al. Eur Heart J Suppl. .

Abstract

Criteria for diagnosis of arrhythmogenic cardiomyopathy (ACM) were first proposed in 1994 and subsequently revised in 2010 and in 2020 by an international task force. According to the last consensus of 2020, ACM is defined as a heart muscle disease affecting right ventricle, left ventricle or both, whose principal pathologic feature is fibrofatty myocardial replacement that impairs systolic ventricular function and predisposes to lethal ventricular arrhythmias. ECG findings not only could help to early recognize affected patients but also could identify the ones with maximum risk of ventricular arrhythmias and sudden cardiac death.

Keywords: Arrhythmias; Arrhythmogenic ventricular cardiomyopathy; Cardiomyopathy; Death; ECG; Prognosis; cardiac; sudden.

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Conflict of interest statement

Conflict of interest: None declared.

Figures

Figure 1
Figure 1
ECG findings of two patients with ARVC. Panel A. ECG performed in a 21-year-old woman shows the classical epsilon wave in lead V1 and T-wave inversion in V1–V6. This patient shows also premature ventricular beats with two LBBB morphologies. Panel B. ECG performed in 43-year-old woman shows epsilon wave in lead V1 and T-wave inversion in V1–V3 leads. LBBB, left bundle branch block.
Figure 2
Figure 2
ECG findings in a patient with ALVC. This 34-year-old man with history of ventricular arrhythmias had a CMR revealing biventricular dilation and a stria LGE pattern with subepicardial distribution, mainly involving the LV lateral wall. This patient showed the ‘classical’ low QRS voltages in limb leads and T-wave inversion in V2–V6 and inferior leads. CMR, cardiac magnetic resonance; LGE, late gadolinium enhancement; LV, left ventricular.
See this image and copyright information in PMC

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