Skip to main page content
U.S. flag

An official website of the United States government

Dot gov

The .gov means it’s official.
Federal government websites often end in .gov or .mil. Before sharing sensitive information, make sure you’re on a federal government site.

Https

The site is secure.
The https:// ensures that you are connecting to the official website and that any information you provide is encrypted and transmitted securely.

Access keys NCBI Homepage MyNCBI Homepage Main Content Main Navigation
Case Reports
. 2023 Mar 31;15(3):e36949.
doi: 10.7759/cureus.36949. eCollection 2023 Mar.

Catheter Embolization of an Orbital Arteriovenous Fistula in a Patient With Wyburn-Mason Syndrome

Balaji Vaithialingam  1 , Swaroop Gopal  2 , Mohammad Sohrab  2
Affiliations
Case Reports

Catheter Embolization of an Orbital Arteriovenous Fistula in a Patient With Wyburn-Mason Syndrome

Balaji Vaithialingam et al. Cureus. .

Abstract

A 24-year-old female presented to the emergency department with swelling of the forehead and oculus sinister. A soft, compressible glabellar swelling with proptosis of the oculus sinister was noted on clinical examination. Cerebral angiography revealed a left medial orbital wall arteriovenous fistula with feeders from the left internal maxillary artery, left superficial temporal artery, and left ophthalmic artery. During the cerebral angiography, a diffuse intracranial venous anomaly and left basal ganglia arteriovenous malformations were also noted. A diagnosis of Wyburn-Mason syndrome was made, and the patient underwent catheter embolization of the orbital arteriovenous fistula. After glue embolization of the left external carotid artery feeders, the patient experienced a 50% reduction in glabellar swelling in the immediate postoperative period. Glue embolization of the left ophthalmic artery feeder was planned after six months during the follow-up period.

Keywords: arteriovenous fistula; arteriovenous malformation; glue embolization; proptosis; wyburn-mason syndrome.

PubMed Disclaimer

Conflict of interest statement

The authors have declared that no competing interests exist.

Figures

Figure 1
Figure 1. Patient with glabellar swelling and oculus sinister proptosis due to orbital arteriovenous fistula
Figure 2
Figure 2. Selective left external carotid angiography (lateral view) showing left maxillary and left superficial temporal artery feeders supplying the left orbital arteriovenous fistula
Figure 3
Figure 3. Selective left internal carotid angiography (lateral view) showing the left ophthalmic artery feeder supplying the left orbital arteriovenous fistula and diffuse nidus in the left basal ganglia
Figure 4
Figure 4. Venous phase of the cerebral angiography (lateral view) showing a diffuse developmental venous anomaly
See this image and copyright information in PMC

References

    1. A case report of Wyburn-Mason syndrome and review of the literature. Dayani PN, Sadun AA. Neuroradiology. 2007;49:445–456. - PubMed
    1. Wyburn-Mason or bonnet-Dechaume-Blanc as cerebrofacial arteriovenous metameric syndromes (CAMS). A new concept and a new classification. Bhattacharya JJ, Luo CB, Suh DC, Alvarez H, Rodesch G, Lasjaunias P. Interv Neuroradiol. 2001;7:5–17. - PMC - PubMed
    1. Cerebral arteriovenous malformation in Wyburn-Mason syndrome. Zeng Y, Fan YC, Liu Y, Wan L. J Pediatr Ophthalmol Strabismus. 2016;53 [Online]:0–7. - PubMed
    1. Retinocephalic vascular malformation: case report. Muthukumar N, Sundaralingam MP. Br J Neurosurg. 1998;12:458–460. - PubMed
    1. The natural history of unruptured intracranial arteriovenous malformations. Brown RD Jr, Wiebers DO, Forbes G, O'Fallon WM, Piepgras DG, Marsh WR, Maciunas RJ. J Neurosurg. 1988;68:352–357. - PubMed

Publication types

LinkOut - more resources