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Case Reports
. 2023 May 15;11(5):e7350.
doi: 10.1002/ccr3.7350. eCollection 2023 May.

A case of Pierre Robin syndrome in a child with no soft palate and complications from pneumonia in Bangladesh

Mohammad Ashraful Amin  1   2 , Taraque Ahamed Shawon  3 , Naushad Khan Shaon  4 , Sabrina Nahin  5 , Jannatul Fardous  6 , Mohammad Delwer Hossain Hawlader  1
Affiliations
Case Reports

A case of Pierre Robin syndrome in a child with no soft palate and complications from pneumonia in Bangladesh

Mohammad Ashraful Amin et al. Clin Case Rep. .

Abstract

Key clinical message: Children with Pierre Robin syndrome (PRS) often have trouble breathing and eating as soon as they are born. If conservative therapy fails to alleviate airway obstruction, surgical surgery may be considered. Patients with PRS require multidisciplinary approaches for treatment.

Abstract: Pierre Robin syndrome is a common craniofacial abnormality that causes glossoptosis and blockage of the upper airway. This renders it difficult to feed, which leads to severe malnutrition. This condition is also often marked by an absence of a soft palate. We mention a newborn with Pierre Robin syndrome with the absence of a soft palate and pneumonia complications, whose impending respiratory failure was treated successfully. To solve the complex problems that these babies and their families are facing, a multidisciplinary approach is needed.

Keywords: Pierre Robin syndrome; congenital defects; feeding problem; micrognathia; pediatrics; pneumonia; soft palate.

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Conflict of interest statement

The authors declare that they have no competing financial interests or personal relationships that could have appeared to influence the work reported in this paper.

Figures

FIGURE 1
FIGURE 1
Chest X‐ray of the patients.
FIGURE 2
FIGURE 2
Pierre Robin syndrome in a child with no soft palate.
See this image and copyright information in PMC

References

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