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. 2023 Sep 1;34(6):e564-e566.
doi: 10.1097/SCS.0000000000009394. Epub 2023 May 29.

Metopic and Sagittal Craniosynostosis in Williams Syndrome

Sarut Chaisrisawadisuk  1 , Inthira Khampalikit  2 , Mark H Moore  3 , Achara Sathienkijkanchai  4
Affiliations

Metopic and Sagittal Craniosynostosis in Williams Syndrome

Sarut Chaisrisawadisuk et al. J Craniofac Surg. .

Abstract

Craniosynostosis has been previously reported in patients with Williams syndrome. Due to the associated significant cardiovascular anomalies, with an attendant increased risk of death under anaesthesia, most patients have been managed conservatively. Here we report the multidisciplinary approach in a 12-month-old female infant with Williams syndrome who has metopic and sagittal craniosynostosis. The child successfully underwent calvarial remodelling procedures, with the clinical outcome demonstrating dramatically improved global development after surgery.

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Conflict of interest statement

The authors report no conflicts of interest.

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